Intracranial immature teratoma of the lateral ventricle: a case report

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Congenital intracranial tumours are very rare and account for 0.5-1.5% of all pediatric brain tumours. [1, 2, 3, 4] According to Sclhembach D et al [4] the most common type of these tumours is teratoma. Teratoma is located predominantly in supratentorial brain and in midline structure such as pineal gland, quadrigeminal plate, walls of the third ventricle, suprasellar region and cerebellar vermis. Its location in the lateral ventricle is extremely rare. We report a case of intracranial immature teratoma in a 2-day-old female presenting with macrocephaly and hydrocephalus which diagnosed as a brain tumour by ultrasound investigation and confirmed at autopsy.

Case report

A 26-year-old healthy primigravida was followed for a normal pregnancy with a normal ultrasonography at 20th week. At 32th week of gestation ultrasound investigation revealed a massive macrocephaly with hydrocephalus due to a right lateral ventricular choroid plexus mass. A week later another Ultrasound scan confirmed the diagnosis and showed tumour growth increase. Because of macrocephaly labour was induced at 34th week with palliative care project for the infant at birth in accordance with family. The fetus was delivered by caesarean section because of failed induction of labour after 48 hours. The newborn weighed 2790g and had a massive macrocephaly her head circumference was 42 cm. The fontanels were enlarged and there were split cranial sutures. Otherwise, the infant had normal appearing body. After delivery, he breathed after a few seconds and cries openly at ten minutes. During the first day, he presented oxygen desaturation many a time and died on the second day after a cardiac arrest.
An autopsy was performed. Cranial bones were extremely thin. A huge tum...

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