“Hypoplastic left heart syndrome accounts for 9% of all critically ill newborns with congenital cardiac disease, causing the largest number of cardiac deaths in the first year of life.(2) ” HLHS is a severe heart defect that is present at birth. HLHS combines different defects that result in an underdeveloped left side of the heart. This syndrome is one of the most challenging and difficult to manage of all of the congenital heart defects. Multiple portions on the left side of the heart are affected including the left ventricle, the mitral and aortic valve, and the ascending aorta. These structures are greatly reduced in size, or completely nonexistent causing the functionality of the left heart to be reduced, or non-functional all together. …show more content…
During pregnancy an echocardiogram of the fetus can be done to produce images of the heart by sending ultrasonic sound waves to the vital organ. These sound waves create an image for the physician to analyze the babies heart function, structure sizes, and blood flow. A positive diagnosis before birth has shown to improve chances of survival, and will allow for appropriate care to be readily available at birth. If a baby is born without being diagnosed with the heart defect, some symptoms previous noted such as low oxygen levels can be suggestive of hypoplastic left heart syndrome. The baby may not display any symptoms or signs for hours after birth because of the openings allowing for blood to be pumped to the rest of the body. However, listening to the babies heart can revel a murmur indicating an irregular flow of blood in the heart. If a murmur is heard, or signs of the defect are observed, diagnostic tests will be ordered and performed. An echocardiogram is still the go-to test once the baby is born to evaluate the heart. The echocardiogram will diagnose the newborn, by revealing the underdeveloped left ventricle, mitral and aortic valve, and the ascending aorta commonly seen in
Hypertrophic Cardiomyopathy, also known as HCM, is a type of heart disease that affects the Cardiac Muscles and Cardiac Muscle cells. This disease occurs if the Cardiac Muscle cells enlarge, which causes the wall of the heart’s ventricles (most often the left ventricle) to thicken. It can also cause stiffness in the ventricles, as well as mitral valve and cellular changes.
Ebstein’s Anomaly is a rare congenital condition, present at birth, in which the tricuspid valve is malformed and the valve itself is not in the correct anatomic place (Mayo Clinic Staff). This anomaly affects the right side of the heart – the tricuspid valve is located too deep into the ventricle, causing a smaller and weaker right ventricle. The space above the decreased right ventricle is made up of atrial tissue and this can be referred to as right ventricle dysplasia or an atrialized right ventricle (Reynolds). Typically the tricuspid valve has three freely moving leaflets, but in Ebstein’s anomaly one or two of those leaflets get fused to the heart walls causing regurgitation. Since the heart does not work as efficiently in those who have this anomaly, the heart usually compensates and becomes enlarged. It...
Of the two representations of the “Tell-Tale Heart”, the live action version is best. The live action was more accurate to the original story than the animated version was. The animated version was mostly for entertainment and got some facts wrong. In the live action, he killed the man in the same way and it had all the narrative of the story. The narrator wasn't Poe, like he was in the animated version. He disposed of the body the same and acted the way the character did in the original book. In the live action, the old man’s eye was completely covered by the film. He also panicked the same way as the book.
First and foremost, Eisenmenger syndrome was initially described in 1897 when German physician, Victor Eisenmenger, reported on a patient with symptoms of dyspnea and cyanosis from infancy that subsequently developed heart failure (Connolly, 2014). The postmortem description was revealed and a ventricular septal defect was discovered (El-Chami et al., 2014a). With that being said, this had been the first time that the link between a large congenital cardiac shunt defect and the development of pulmonary hypertension had ever been noted (El-Chami et al., 2014b). The normal heart has four chambers. The two upper chambers are separated from each other by the atrial septum (NORD, 2014a). The two lower chambers are known as ventricles and are separated from each other by the ventricular septum (NORD, 2014b).
Cardiomyopathy, by definition, means the weakening of the heart muscle. The heart is operated by a striated muscle that relies on the autonomic nervous system to function. Cardiomyopathy is diagnosed in four different ways based on what caused the illness and exactly what part of the heart is weakened. The four main types of cardiomyopathy are dilated cardiomyopathy, hypertrophic cardiomyopathy, restrictive cardiomyopathy, and arrhythmogenic right ventricular dysplasia. One other category of cardiomyopathy that is diagnosed is “unclassified cardiomyopathy.” Unclassified cardiomyopathy is the weakening of the heart that does not fit into the main four categories.
Eisenmenger Syndrome (ES) is a heart defect that was first giving the name in 1897 (Fukushima, 2015). This syndrome happens when the birth defect is not treated before the lungs’ arteries become damaged. Eisenmenger Syndrome is named after Victor Eisenmenger a man who had a patient who showed symptoms such as, breathing complications and skin that was turning a bluish color. The autopsy of this patient lead him to discover a ventricular septal defect [VSD] (El-Chami, 2014), that causes a hole in the wall on the right and left ventricular. This is the defect that begins when signaling for pulmonary artery hypertension, which progresses into more advanced stages of ES. This birth defect eventually causes patients to have various
Hypertrophic Cardiomyopathy: Effects on Young Athletes Alyssa Trimm 130568370 Wilfrid Laurier University Dr. Kalmar KP 122 Section A
During a physical examination, a specialist may hear a heart murmur which will prompt a referral to a pediatric cardiologist for an analysis. Diagnostic testing will vary by the child’s age, clinical condition, and institutional preferences. Such test may incorporate a chest X-ray, electrocardiogram, echocardiography and cardiac catheterization. A chest X-ray uses unseen X-ray beams to cr...
Tetralogy of Fallot is a congenital heart disease which involves four different heart defects in one. The four different heart defects are a large ventricular septal defect (VSD), Pulmonary Stenosis, Right ventricular hypertrophy, and an overriding aorta. These congenital defects change the normal flow of blood thro...
Hypertrophic cardiomyopathy is an inherited disease that affects the cardiac muscle of the heart, causing the walls of the heart to thicken and become stiff. [1] On a cellular level, the sarcomere increase in size. As a result, the cardiac muscles become abnormally thick, making it difficult for the cells to contract and the heart to pump. A genetic mutation causes the myocytes to form chaotic intersecting bundles. A pathognomonic abnormality called myocardial fiber disarray. [2,12] How the hypertrophy is distributed throughout the heart is varied. Though, in most cases, the left ventricle is always affected. [3] The heart muscle can thicken in four different patterns. The most common being asymmetrical septal hypertrophy without obstruction. Here the intraventricular septum becomes thick, but the mitral valve is not affected. Asymmetrical septal hypertrophy with obstruction causes the mitral valve to touch the septal wall during contraction. (Left ventricle outflow tract obstruction.) The obstruction of the mitral valve allows for blood to slowly flow from the left ventricle back into the left atrium (Mitral regurgitation). Symmetrical hypertrophy is the thickening of the entire left ven...
(Slide 2) What is Cardiomyopathy? If we break down the word we can see “Cardio” which means of the heart, “myo” which means muscle, and “pathy” which means disease, therefore cardiomyopathies are diseases of the heart muscle. (Slide 3) There are 3 main types of cardiomyopathies; hypertrophic, dilated, and restrictive. I will only be discussing dilated cardiomyopathy, which is characterized by the enlargement of the hearts chambers with impaired systolic function. It is estimated that as many as 1 of 500 adults may have this condition. Dilated cardiomyopathy is more common in blacks than in whites and in males than in females. It is the most common form of cardiomyopathy in children and it can occur at any age (CDC).
Why is it that by 21 days into the fetal development the baby's heart begins to
This is called newborn screening. Within newborn screening there three test normally given. This screening occurs not long after birth and can provide details about developmental, genetic and metabolic disorders. Two test completed in the screening are for hearing loss and for critical congenital heart disease (CCHD). The hearing test is completed by placing either a tiny earpiece of microphone in the infants’ ear with a sound playing to see whether the infant responds or not. Another way the test is given is by using tiny earphones and electrodes that are placed on the infant’s head to detect the brains response to sound (National Institute of Child Health and Human Development, 2015). The other tests that may be performed is the CCHD screen which the amount of oxygen in an infant’s blood is measured. In order to do this a sensor is placed on the infants’ skin for a couple of minutes, while the sensor measures the level of oxygen in the blood. Within in newborn screening there is also another tests which is the most important
In the fetal circulation, the right and left ventricles work in a parallel circuit. The ductus venosus, foramen ovale, and ductus arteriosus are three cardiovascular structures that are important for maintaining this circulation. The umbilical vein carries relatively well-oxygenated blood from the placenta to the IVC through the ductus venosus, where it partially mixes with poorly oxygenated IVC blood from the lower part of the fetal body. When it reaches the right atrium, oxygenated blood is preferentially shunted across the foramen ovale and then enters the left atrium, where it mixes with blood from the pulmonary veins before entering the left ventricle. From the LV, the ascending aorta sends fully oxygenated blood to the coronary arteries, the head, and the upper extremities. Only a small portion of the LV cardiac output streams through the aortic arch and supplies flow to the thoracic aorta.
Technology has had a very prominent influence on electronic fetal monitoring since its appearance in the 1960’s and 1970’s. For many years, fetal monitoring was simply done by listening to a fetal heartbeat through a stethoscope. Dramatic changes in the heartbeat, such as a long period or a drop in the rate or intensity, could be detected,. Now, not only is the electronic fetal monitor used on the outside of the womb by strapping electrodes to the mother’s abdomen but electrodes can also be inserted during the first stage of labor and placed directly on the baby’s head. With advanced technologies such as this the acidity of the infant’s blood as well as the heart rate can be measured.