Essay PreviewMore ↓
Life threatening condition
Common in Caucasian
• Affects the production of mucus, sweat, digestive juices and infertility
Nurses deal with many different types of illnesses and conditions. There are different kinds of genetic diseases. One of the most common life threatening conditions is cystic fibrosis. According to the US Cystic Fibrosis Foundation, “projected life expectancy for the patients has increased from 31 to 37 years over the past decade” (O’Sullivan & Freedman, 2009, p. 1891). Cystic Fibrosis inherits two faulty genes for the disease from both parents. This condition is most common in white people of Northern European ancestry. It affects the production of mucus, sweat, digestive juices and infertility. The mucus becomes thick and sticky, blocking the airways, which leads to recurrent infections. Cystic fibrosis causes a person’s sweat to become salty, which upsets the balance of minerals in the blood and causes health problems. The thick mucus can also block the ducts in the pancreas. The pancreas makes digestive enzymes which helps break down food. Without the enzymes, the intestines cannot absorb fats and proteins that may cause bulky stools, intestinal gas, a swollen belly from constipation and pain and/or discomfort. Men and women may experience infertility as a result of having cystic fibrosis.
• Affects the production of mucus
• Decreases sweat, digestive juices
• Increases infertility
• Cystic fibrosis affects the production of mucus, sweat, digestive juices and infertility. The mucus becomes thick and sticky, blocking the airways, which leads to recurrent infections. Cystic fibrosis causes a person’s sweat to become salty, which upsets the balance of minerals in the blood and causes health problems. The thick mucus can also block the ducts in the pancreas. The pancreas makes digestive enzymes which helps break down food. Without the enzymes, the intestines cannot absorb fats and proteins that may cause bulky stools, intestinal gas, a swollen belly from constipation and pain and/or discomfort. Men and women may experience infertility as a result of having cystic fibrosis.
• SLIDE 3
Impacts on Development
• Self esteem
• Lack of sleep
• Adolescence is a time of many challenges including physical, intellectual and emotional challenges. Developmental issues face all teens but the impact is elevated for those with cystic fibrosis. Puberty is delayed with cystic fibrosis, which can affect a child’s self-esteem and elevate their sense of being different.
How to Cite this Page
"Cystic Fibrosis Presentation." 123HelpMe.com. 17 Jun 2019
Need Writing Help?
Get feedback on grammar, clarity, concision and logic instantly.Check your paper »
- As mentioned previously, cystic fibrosis is one of the most severely life-shortening genetic diseases today. Although people eventually succumb to this disease process, medicine has made great strides in increasing the life expectancy to over 40 years since the 1940s (Kreindler and Miller, p1221). Nearly half of the cystic fibrosis patients are over 18 years old. Because of this, it should be a priority for these patients to be transferred from pediatric CF centers to adult care CF centers. Adults with cystic fibrosis tend to have more complications related to the affected systems such as liver failure and diabetes.... [tags: Medicine, Health care, Health care provider]
1578 words (4.5 pages)
- Introduction Cystic fibrosis is an inherited disease that ultimately leads to death. It affects every racial group worldwide, but its prevalence varies from country to country. In those with cystic fibrosis, the lungs and digestive system are primarily affected by the disease. With the new developments in treatment and management, the 50 percent survival rate from the 1970’s has greatly improved, allowing patients to continue to live their lives longer than ever expected in the past. The new developments in prevention of exacerbations, therapy drugs and methods to preserve lung function have done great things to help patients extend their lives.... [tags: Diseases, Disorders]
1965 words (5.6 pages)
- Cystic Fibrosis Cystic Fibrosis is a genetic disease that affects many people today. It takes over a person’s whole life to survive this disease. To survive, people who suffer with Cystic Fibrosis need constant care of this disease. Cystic fibrosis is disorder that is inherited and causes severe damage to the lungs and digestive system. Cystic fibrosis changes the cells that make mucus, sweat and digestive juices. These fluids that are secreted are normally thin and slippery. A defective gene causes the secretions to become thick and sticky.... [tags: Cystic fibrosis, Genetics, Digestion, Pneumonia]
809 words (2.3 pages)
- The effects of cystic fibrosis can be broken down to a micro-perspective investigation in both the genotype, the encoding of the DNA, and the phenotype, the expression of DNA to trait. A precursor to the expression of cystic fibrosis, is through the inheritability pattern of cystic fibrosis from both parents. Cystic fibrosis is an autosomal recessive disease, meaning in the DNA of each parent, each had one copy of these recessive trait which is not expressed through them. However, with both parents being carriers, the offspring has a 25% chance of inheriting cystic fibrosis, a 25% chance of inheriting non-mutated genes and a 50% chance of being a carrier of the cystic fibrosis gene (Mayer-Ha... [tags: Mutation, DNA, Gene, Cystic fibrosis]
992 words (2.8 pages)
- Your child is under weight, has greasy, smelly diarrhea, a chronic cough and seems to always be getting pneumonia. He wheezes when he breathes and has impaired exercise ability. He seems to never being growing to the average size of his peers and his skin is very salty (5). The doctor’s first instinct should be to test your child for a disease called cystic fibrosis. Cystic fibrosis is a disease, which causes the mucus in your body to be thicker in some areas. The most affected areas are the lungs and digestive system.... [tags: Digestion, Cystic fibrosis, Pancreas, Cell]
1245 words (3.6 pages)
- Cystic Fibrosis Introduction Cystic fibrosis (CF) is an inherited chronic disease that must be carried by both parents in order to for the person to suffer from it. When two parents who are carriers have a child there is a 25 percent chance of having a child with CF and when one parents has CF and one parent is a carrier, there is a 50 percent chance of having a child with CF This disease affects organs such as the liver, lungs, pancreas, and intestines. This disease disrupts the body’s salt balance leaving too little salt and water on the outside of cells which makes the thin mucus that protects the linings of the airways, digestive system, reproductive system, and other organs and tissues... [tags: Cystic fibrosis, Pulmonology, Asthma]
1312 words (3.7 pages)
- Cystic fibrosis is a genetically inherited disease due to a mutation in the CFTR gene. This disease causes life changing health complications that affect many organs within the human body. There is always ongoing research for this disease to discover better treatment options that are more effective and possibly find a cure to reverse the mutated gene. The Cystic fibrosis transmembrane conductance regulator gene (CFTR) is responsible for providing the instructions to help make the protein that produces mucus in the body.... [tags: Cystic fibrosis, Genetics, Mutation, Asthma]
1836 words (5.2 pages)
- Cystic Fibrosis Cystic Fibrosis is a lung disease caused by a mutated gene. This gene called the CFTR gene causes a protein to not allow salt or water to flow through a cell properly. This produces a thick, sticky mucus to collect in the lungs and other organs. In order for a person to get this disease, the parents both have to be carriers of this disease. Usually a person is diagnosed within the first year of life. In the United States 1 in 2,500 to 3,500 Caucasian Americans, 1 in 17,000 African-Americans, and 31,000 Asian-Americans will have this disease.... [tags: Cystic fibrosis, Pulmonology, Asthma]
1397 words (4 pages)
- Overcoming Proteasomes: One Step Closer to a Cure for Cystic Fibrosis Take a deep breath and consider how easy it was to do so. Now picture struggling and gasping for air everyday; normal, easy tasks to the average person prove to be quite challenging to a patient of cystic fibrosis. Scientists have always been daunted by this fatal genetic disease that affects the body by excreting a “thick mucus” in the lungs, making breathing difficult and blocking the “ducts” leading from the pancreas, causing “poor digestion of food” (1).... [tags: Proteasomes Cystic Fibrosis]
1399 words (4 pages)
- Abstract: The main goal of this paper is to explain what Cystic Fibrosis is and also to explain what the causes of Cystic Fibrosis are. Cystic Fibrosis is caused by a mutation in a gene called Cystic Fibrosis Transmembrane Conductance Regulator (CFTR). Cystic Fibrosis is known as one of the most common life-shortening disease. More that 1,000 mutations in the CFTR gene have been found in people with Cystic Fibrosis. Most of these mutations change single protein amino acids in the CFTR protein and it deletes a small amount of DNA from the CFTR gene.... [tags: Biology Medical CFTR Cystic Fibrosis]
717 words (2 pages)
• Identity Versus Role Confusion
- Dramatic physiological changes
- Preoccupation with appearance and body image
- Acquiring sense of identity
Erikson’s theory of cognitive development can be used to develop nursing interventions for an adolescent suffering from cystic fibrosis. According to Erikson’s theory an adolescent would be in the identity versus role confusion stage. During this stage adolescents reach sexual maturity. They are also very body conscious and concerned with their appearance more than ever before. At this stage they begin to develop a sense of identity. “Acquiring a sense of identity is essential for making adult decisions such as choice of vocation or marriage partner”
(Potter & Perry, 2005, p. 161).
Nursing Interventions – Education
- Help establish a sense of identity
- Provide adequate information
- Establish confidentiality
Adolescents suffer from embarrassment in silence. They are afraid to ask questions about all the challenges they are going though. Nurses need to present information proactively and speak alone with the teenager to help them feel comfortable with asking questions. In doing so the nurse can utilize Erikson’s theory that adolescents are developing their own sense of identity and making adult decisions. By providing adolescents with adequate information regarding their condition and treatment options they will be able to contribute to their plan of care and make decisions regarding their health. “Throughout their time in care, healthcare professionals should empower young adults and promote their independence using various strategies, for example providing information, considering their opinion” (Al-Yateem & Moyola, 2013, p. 33). The concept of confidentiality needs to be explained to the adolescent. Establishing confidentiality helps develop a sense of trust between the patient and nurse. It allows for a more open and honest discussion and will help in developing a good plan of care.
• Nursing Interventions – Encouraging Active Lifestyle
Honest feedback regarding body image
• Physical activity
• Benefits and barriers
• Physical activity and exercise are recommended for management of cystic fibrosis. Adolescents with CF are less active than their peers. This may have a negative effect on their appearance and body image. By utilizing Erikson’s theory we can address the adolescents concerns about body image by being honest regarding what changes to expect during treatment for cystic fibrosis. By being honest with what to expect, adolescents can begin preparing themselves for these changes. Nursing interventions to assist with body image and appearance should include promoting exercise. Promoting physical activity and exercising regularly as part of the management of cystic fibrosis is important. “Regular aerobic exercise enhances cardiovascular fitness, enhances airway clearance, slows declines in lung function, and improves body mass” (Swisher & Erickson, 2008, p. 107). There are benefits and barriers when promoting an active lifestyle to adolescents with CF. The barriers are physical discomfort such as muscle soreness, fatigue, joint pain and increased heart rate. Coughing and shortness of breath are also part of the problem. The important benefits are delayed onset of dyspnea, maintenance of bone density, enhanced cellular immune response, and increased feelings of well-being. The team of clinicians and caregivers needs to create an individual plan for the adolescent with CF. It is important to education and promote physical activity and exercise as a part of lifestyle for maintaining both overall health and for improving lung symptoms and energy levels.
Nursing Interventions - Nutrition
- Long-term survival
- Maintain lung health
- Encourage higher, healthy caloric intake
Dramatic physical changes are seen during adolescence. According to Erikson, adolescents are very concerned with their appearance and when suffering from cystic fibrosis they may have a poor appetite, which will affect their physical growth and development. Informing adolescents that maintaining a healthy diet will help them with their appearance will encourage them to eat more. “The benefits of maintaining good nutrition in regard to long-term survival and lung health cannot be overstated” (O’Sullivan & Freedman, 2009, p. 1899). The mucus from the CF can block the body from absorbing nutrients from food. Explain to the teenager that eating a lot of calories is part of living. Fortunately, most popular foods are also high in calories. The trick is to still eat healthy food with high protein, vegetables, fruits and dairy. Let the teens invite their friends over for snacks or meals. It will make getting calories more fun with friends. Supplements such as pancreatic enzymes are encouraged for those patients with less than optimum growth.
There are many types of treatments for cystic fibrosis. The focus for treatments is to keep the lungs clear and infection free. Antibiotics are often used to help treat and prevent the onset of lung infections. Bronchodilators are used to keep the airway clear by helping the muscles located around the bronchial tubes to relax. Breathing devices are also used to help exercise and strengthen the lungs. Sometimes surgical procedures may be necessary to help clear the airway and improve breathing. Procedures such as an endoscopy and lavage can be performed to suction out excessive mucus build up.
Evaluation of Nursing Interventions
There are ways to evaluate the nursing intervention when taking care of adolescents with cystic fibrosis. At each physical exam, the height and weight should be measured including calculating their body-mass index (BMI). By doing this regularly, the nurse can access if there is a decrease in BMI or stunting of growth and if necessary provide the adolescent with nutritional counseling. Good nutritional well-being has a positive correlation with good healthy lungs in cystic fibrosis. If the nutritional status is poor, supplements should be strongly considered. Patients with pancreatic insufficiencies need supplements such as pancreatic enzymes. CF patients have difficulty digesting foods due to thick mucus that can clog the ducts of the pancreas creating poor digestion. Pancreatic enzymes helps digest and absorb the food in patients with CF. When CF adolescents get hospitalized, nurses need to find out how much physical activity they participate in or how often they incorporate exercises into their daily routines. Identifying the barriers and communicating with the CF team to find ways to help the individual in promoting an active life style into their daily routines helps decrease hospitalization. Nurses need to identify ineffective communication. In order to improve the ability to communicate, nurses need to educate and increase the knowledge of multiple needs of the adolescents with CF. Providing reassurance enhances communication and understanding regarding their fears and anxieties. Having a team approach allows the adolescent to communicate about specific problems. Members of a multidisciplinary CF team include doctors, physiotherapists, dieticians, social workers, and nurses.